Review  |   December 2011
Audiologic Management of Auditory Neuropathy Spectrum Disorder in Children: A Systematic Review of the Literature
Author Affiliations & Notes
  • Patricia Roush
    University of North Carolina, Chapel Hill
  • Tobi Frymark
    American Speech-Language-Hearing Association, Rockville, MD
  • Rebecca Venediktov
    American Speech-Language-Hearing Association, Rockville, MD
  • Beverly Wang
    American Speech-Language-Hearing Association, Rockville, MD
  • Correspondence to Tobi Frymark: tfrymark@asha.org
  • Editor: Sheila Pratt
    Editor: Sheila Pratt×
  • Associate Editor: Ruth Litovsky
    Associate Editor: Ruth Litovsky×
Hearing Disorders / Hearing Aids, Cochlear Implants & Assistive Technology / Audiologic / Aural Rehabilitation / Review
Review   |   December 2011
Audiologic Management of Auditory Neuropathy Spectrum Disorder in Children: A Systematic Review of the Literature
American Journal of Audiology December 2011, Vol.20, 159-170. doi:10.1044/1059-0889(2011/10-0032)
History: Accepted 18 Jul 2011 , Received 04 Aug 2010 , Revised 07 Mar 2011
American Journal of Audiology December 2011, Vol.20, 159-170. doi:10.1044/1059-0889(2011/10-0032)
History: Accepted 18 Jul 2011 , Received 04 Aug 2010 , Revised 07 Mar 2011

Purpose: This review summarizes current evidence related to the audiologic management of children with auditory neuropathy spectrum disorder (ANSD).

Method: A systematic search of the literature was conducted in 25 electronic databases (e.g., PubMed, CINAHL, and ERIC) using key words such as auditory neuropathy,auditory neuropathy spectrum disorder,auditory neuropathy/dyssynchrony, and hearing loss. Eighteen studies met the inclusion criteria by addressing 1 or more of 8 clinical questions. Studies were evaluated for methodological quality, and data regarding participant, intervention, and outcome variables are reported.

Results: Fifteen of the 18 studies addressed the use of cochlear implantation, and 4 addressed conventional acoustic amplification. All participants demonstrated improved auditory performance; however, all 18 studies were considered exploratory, and many had methodological limitations.

Conclusion: The clinical evidence related to intervention for ANSD is at a very preliminary stage. Additional research is needed to address the efficacy of acoustic amplification and cochlear implantation in children with ANSD and the impact of this disorder on developmental outcomes.

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